Order Code KSQNU Keratan Sulfate Quantitative, Urine
Useful For
Monitoring the pharmacodynamic effects of enzyme replacement therapy for Morquio A (MPS IVA)
Method Name
Liquid Chromatography-Tandem Mass Spectrometry (LC-MS/MS)
Reporting Name
Keratan Sulfate Quantitative, USpecimen Type
UrineNecessary Information
Patient’s age is required.
Specimen Required
Supplies: Plastic, Urine Tubes, 10 mL (T068)
Specimen Volume: 1 mL
Collection Instructions:
1. Collect a random urine collection (early morning preferred).
2. Immediately freeze specimen.
Specimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Frozen | 365 days |
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability. |
Reference Values
0-12 months: ≤2.50 mg/mmol creatinine
13-24 months: ≤2.00 mg/mmol creatinine
25 months-4 years: ≤1.50 mg/mmol creatinine
5-10 years: ≤1.00 mg/mmol creatinine
11-18 years: ≤0.80 mg/mmol creatinine
>18 years: ≤ 0.50 mg/mmol creatinine
Day(s) and Time(s) Performed
Varies
Performing Laboratory

Test Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. This test has not been cleared or approved by the U.S. Food and Drug Administration.CPT Code Information
83864
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
KSQNU | Keratan Sulfate Quantitative, U | 92806-9 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
64712 | Keratan Sulfate Quantitative, U | 92806-9 |
Forms
Biochemical Genetics Patient Information (T602) in Special Instructions