Order Code LAB937 Orotic Acid, Random, Urine
Additional Codes
Mayo Test Code: OROT
Reporting Name
Orotic Acid, UUseful For
Evaluation of the differential diagnosis of hyperammonemia and hereditary orotic aciduria
Sensitive indicator of ornithine transcarbamylase (OTC) activity after administration of allopurinol or a protein load to identify OTC carriers
Performing Laboratory

Specimen Type
UrineNecessary Information
Patient's age is required.
Specimen Required
Supplies: Urine Tubes, 10 mL (T068)
Container/Tube: Plastic, 10-mL urine tube
Specimen Volume: 3 mL
Collection Instructions:
1. Collect a random urine specimen.
2. No preservative needed.
Specimen Minimum Volume
2 mL
Specimen Stability Information
Specimen Type | Temperature | Time |
---|---|---|
Urine | Frozen | 90 days |
Reference Values
≤6 years: ≤4 mmol/mol creatinine
7-18 years: ≤3 mmol/mol creatinine
≥19 years: 5 mmol/mol creatinine
Day(s) Performed
Tuesday, Thursday
CPT Code Information
83921
Method Description
Diluted, filtered urine is mixed with an internal standard mixture and analyzed for orotic acid by liquid chromatography-tandem mass spectrometry. The ratio of the extracted peak area of orotic acid to the added internal standard is used to calculate the concentration present in the sample.(la Marca G, Casetta B, Malvagia S, et al. Implementing tandem mass spectrometry as a routine tool for characterizing the complete purine and pyrimidine metabolic profile in urine samples. J Mass Spectrom. 2006;41[11]:1442-1452; Monostori P, Klinke G, Hauke J, et al. Extended diagnosis of purine and pyrimidine disorders from urine: LC MS/MS assay development and clinical validation. PLoS One. 2019;14[2]:e0212458. doi:10.1371/journal.pone.0212458)
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Method Name
Liquid Chromatography Tandem Mass Spectrometry (LC-MS/MS)
Forms
1. Biochemical Genetics Patient Information (T602)
2. If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.